Sturge-Weber syndrome presenting with intractable seizures
نویسندگان
چکیده
منابع مشابه
Teaching NeuroImages: Sturge-Weber syndrome presenting in a 58-year-old woman with seizures.
A 58-year-old woman with a history of migraine presented with headache, aphasia, right homonymous hemianopsia, and right hemiparesis, followed by 2 seizures. On examination, she was noted to have a facial angioma (figure 1) that was present from childhood. MRI findings (figure 2, A–C) were consistent with leptomeningeal angiomatosis, making the diagnosis of Sturge-Weber syndrome. Sturge-Weber s...
متن کاملAngiodysplastic Sturge Weber syndrome.
Accepted 19 November 2017 DesCripTion A 3-year-old boy presented with global developmental delay, abnormal craniofacial growth and left focal seizures since infancy. He was the first child of a non-consanguineous couple with unremarkable perinatal period. Family history was non-contributory. On examination, he had macrocephaly (head circumference 55 cm, >3 z-score), extensive port-wine stain di...
متن کاملSturge-Weber Syndrome
Sturge-Weber syndrome (SWS) is a neurocutaneous syndrome, characterized by the association of facial port-wine hemangiomas in the trigeminal nerve distribution area, with vascular malformation(s) of the brain (leptomeningeal angioma) with or without glaucoma. Herein, we reported Sturge-Weber syndrome in a 50-year-old man, who presented port-wine hemangiomas and epilepsy. In this case, the patie...
متن کاملThe Sturge-Weber Syndrome
The association of vascular nxvi of the face, predominantly unilateral in distribution, with homolateral changes in the cerebral cortex, has long been of interest to clinicians. The first case4 of this disorder was presented by W. Allen Sturge to the Clinical Society of London in 1879. Weber5 called attention to the characteristic roentgenological features of this disease in 1922, and in 1934. ...
متن کاملSturge-Weber syndrome with bilateral intracranial calcification.
Four children affected by Sturge-Weber syndrome and demonstrating bilateral intracranial calcification are described, bringing up to 21 the number of similar reported cases. The frequency of bilateral hemisphere involvement in this syndrome is not known, but it might be as high as 15%. If present, neurosurgical intervention is, in our opinion, contraindicated.
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ژورنال
عنوان ژورنال: Journal of Institute of Medicine
سال: 2010
ISSN: 1993-2979
DOI: 10.3126/joim.v32i1.4002